Abstract
We present a case of patient with hypertrophic cardiomyopathy and an anomalous right coronary artery with left main artery origin and an interarterial course. The coexistence of these two different entities is extremely rare but of major clinical significance because both are associated with an increased risk of sudden cardiac death. In addition, a review of the literature comprising 14 other cases with this combination is provided.
Zusammenfassung
Vorgestellt wird ein Patient mit hypertropher Kardiomyopathie und einer anomalen A. coronaria dextra mit Ursprung in der linken Hauptarterie und interarteriellem Verlauf. Dass diese beiden nosologischen Entitäten zusammen auftreten, ist extrem selten, doch die klinische Relevanz ist hoch, denn bei beiden ist das Risiko für einen plötzlichen Herztod erhöht. Neben dem vorgestellten Patienten wird auch die Literatur zu den anderen 14 Patienten mit diesen Erkrankungen besprochen.
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Efthimiadis, G., Theofilogiannakos, E., Gossios, T. et al. Hypertrophic cardiomyopathy associated with an anomalous origin of right coronary artery. Herz 38, 427–430 (2013). https://doi.org/10.1007/s00059-012-3713-y
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DOI: https://doi.org/10.1007/s00059-012-3713-y