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Anomalous Aortic Origin of a Coronary Artery: Clinical and Surgical Perspective

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Ischemic Heart Disease

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Abstract

Anomalous aortic origin of a coronary artery predisposes pediatric patients to myocardial ischemia. This rare condition is a leading cause of sudden cardiac death. General pediatricians face challenges when diagnosing this anomaly, and they should pay particular attention to the recurrence of exercise-related syncope without prodromal symptoms, chest pain, and dyspnea. An accurate transthoracic echocardiogram with Doppler color flow mapping is the best method to use to identify anomalous origin. In this chapter, we describe this rare congenital abnormality.

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Abbreviations

AAOCA:

Anomalous aortic origin of a coronary artery

CA:

Coronary artery

SCD:

Sudden cardiac death

ALCA:

Anomalous left coronary artery

ARCA:

Anomalous right coronary artery

LM:

Left main

TTE:

Transthoracic echocardiography

CTA:

Computed tomography angiography

cMRI:

Cardiac magnetic resonance imaging

sNPI:

Stress nuclear perfusion imaging

FFR:

Fractional flow reserve

sCMR:

Stress cardiac magnetic resonance

IVUS:

Intravascular ultrasound

EST:

Exercise stress test

TAR:

Transection and reimplantation

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  1. Ospedale del cuore “G. Pasquinucci”, Massa, Italy

    Chiara Marrone & Duccio Federici

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  1. Chiara Marrone
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Correspondence to Duccio Federici .

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  1. Department of Adult Cardiac Surgery, Ospedale del cuore “G. Pasquinucci", Massa, Italy

    Giovanni Concistrè

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Marrone, C., Federici, D. (2023). Anomalous Aortic Origin of a Coronary Artery: Clinical and Surgical Perspective. In: Concistrè, G. (eds) Ischemic Heart Disease. Springer, Cham. https://doi.org/10.1007/978-3-031-25879-4_21

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