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Anomalous Aortic Origin of Coronary Arteries Data from the Registries

Registries for Anomalous Aortic Origin of Coronary Arteries

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Congenital Anomalies of Coronary Arteries

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Abstract

Anomalous aortic origin of coronary arteries represents a rare clinical condition, with some anatomycal variants being the second cause of unexpected and sudden death in children and adolescents. Single-center reports are limited by small dimension of cohorts and short follow-up times, which do not allow the formulation of real evidence-based recommendations. Multicenter registries may work as organized systems that use observational study methods to collect uniform data from different institutions, increasing the number of cases and helping in prospective collection of patients and information.

To date, two multicenter registries (one northern American, and the other European) are active. Born as retrospective databases, they have been upgraded to prospective registries. From these experiences, it has been demonstrated on a larger scale that surgery for anomalous aortic origin of coronary arteries, mostly by means of the unroofing procedure, is safe, with very low early and medium-term mortality. Furthermore, surgery seems to be effective in resuming myocardial ischemia and it allows patients to escape from physical activity restrictions. However, surgery carries a not negligible risk of complications and reinterventions, which are present also at short follow-up times. A constant updating of these registries is mandatory to investigate the real durability and safety of surgical correction of anomalous aortic origin of coronary arteries.

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Abbreviations

AAOCA:

Anomalous aortic origin of coronary artery

AAOLCA:

Anomalous aortic origin of left coronary artery

AAORCA:

Anomalous aortic origin of right coronary artery

SCD:

Sudden cardiac death

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Authors and Affiliations

  1. Pediatric and Congenital Cardiac Surgery, Department of Cardio-thoracic, Vascular Sciences and Public Health, University of Padova, Medical School, Padova, Italy

    Massimo A. Padalino & Matteo Ponzoni

  2. UOC Cardiochirurgia Pediatrica e Cardiopatie Congenite, Centro “Vincenzo Gallucci”, Padova, Italy

    Massimo A. Padalino

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  1. Massimo A. Padalino
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  2. Matteo Ponzoni
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Correspondence to Massimo A. Padalino .

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Editors and Affiliations

  1. Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Hospital, Rome, Italy

    Gianfranco Butera

  2. Cardiac Surgery Unit, Policlinico San Donato, SAN DONATO MILANESE, Milano, Italy

    Alessandro Frigiola

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Padalino, M.A., Ponzoni, M. (2023). Anomalous Aortic Origin of Coronary Arteries Data from the Registries. In: Butera, G., Frigiola, A. (eds) Congenital Anomalies of Coronary Arteries. Springer, Cham. https://doi.org/10.1007/978-3-031-36966-7_18

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  • DOI: https://doi.org/10.1007/978-3-031-36966-7_18

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